XVIII - Aortic involvement
Arterial (aorta, limb) vasoconstriction and/or ischemia, acute
Last update 17/06/2026
May involve the aorta or limb arteries causing renal, bowel, limb, brain and/or coronary ischemia
XVIII - Aortic involvement
Last update 17/06/2026
May involve the aorta or limb arteries causing renal, bowel, limb, brain and/or coronary ischemia
I. Cardiac arrhythmia(s)/dysrhythmia(s) (AF, VT, VF, TdP) - QTc prolongation)
I.a Cardiac arrhythmias or dysrhythmias (AF, VT, VF, TdP)
III. Myocardial ischemia - Coronary artery disease
III.a Coronary artery disease (acute) - Myocardial ischemia/infarction
XIV. Pleural involvement
XIV.j Black pleural effusion
XVIII. Aortic involvement
XVIII.c Arterial (aorta, limb) vasoconstriction and/or ischemia, acute
III. Myocardial ischemia - Coronary artery disease
III.a Coronary artery disease (acute) - Myocardial ischemia/infarction
XI. Pulmonary vasculopathies
XI.a Pulmonary arterial hypertension
XII. Pericardial involvement
XII.n Pleuropericarditis - Pleuropericardial effusion (ANA unknown or negative)
XIV. Pleural involvement
XIV.a Pleural effusion (uni or bilateral) (can accompany ILD induced by the drug)
XVI. Hemorrhage - Bleeding - Hematoma(s)
XVI.e Alveolar hemorrhage (AH), diffuse AH (DAH)
XVI. Hemorrhage - Bleeding - Hematoma(s)
XVI.i Hemoptysis
XVIII. Aortic involvement
XVIII.c Arterial (aorta, limb) vasoconstriction and/or ischemia, acute
XX. Vasculitis
XX.d Vasculitis, pulmonary (w/wo AH), extrathoracic, or systemic: ANCA-positive
XXVIII. Large airway involvement
XXVIII.p Nasal, palatal and/or pharyngeal pathology
XXXI. Eye catchers
XXXI.h Midline destructive lesions
XXXVI. Autoimmune syndromes - Systemic reactions or conditions
XXXVI.s Dual MPO-/PR3-ANCA systemic disease/vasculitis or pseudovasculitis
XXXVI. Autoimmune syndromes - Systemic reactions or conditions
XXXVI.t Pneumorenal syndrome (w/wo ANCAs)
XXXVI. Autoimmune syndromes - Systemic reactions or conditions
XXXVI.u Pulmonary vasculitis or capillaritis
XXXVIII. Miscellaneous - Varia
XXXVIII.d Death following exposure or poisoning
XXXVIII. Miscellaneous - Varia
XXXVIII.q Myopathy-Myositis-Polymyositis
XXXVIII. Miscellaneous - Varia
XXXVIII.y Neutropenia, agranulocytosis (w/wo infection/sepsis)