XXXVI - Autoimmune syndromes - Systemic reactions or conditions
Dual MPO-/PR3-ANCA systemic disease/vasculitis or pseudovasculitis
Last update 17/06/2026
XXXVI - Autoimmune syndromes - Systemic reactions or conditions
Last update 17/06/2026
XII. Pericardial involvement
XII.b Pericardial effusion (w/wo tamponade)
XII. Pericardial involvement
XII.e Constrictive pericarditis - Pericardial thickening
XII. Pericardial involvement
XII.g Pleural/pericardial effusion, ANA positive (DI lupus)
XII. Pericardial involvement
XII.n Pleuropericarditis - Pleuropericardial effusion (ANA unknown or negative)
XV. Chest pain
XV.e Pleuritis (can cause chest pain)
XVI. Hemorrhage - Bleeding - Hematoma(s)
XVI.e Alveolar hemorrhage (AH), diffuse AH (DAH)
XVI. Hemorrhage - Bleeding - Hematoma(s)
XVI.g Alveolar hemorrhage, diffuse (ANCA-positive/-related)
XX. Vasculitis
XX.c Vascultis (pulmonary, extrathoracic or systemic) - ANCA status unknown or negative
XX. Vasculitis
XX.d Vasculitis, pulmonary (w/wo AH), extrathoracic, or systemic: ANCA-positive
XXII. Acute respiratory/cardiorespiratory failure
XXII.b Acute lung injury - ARDS
XXIV. Interstitial lung disease - Pulmonary infiltrates - Pulmonary fibrosis
XXIV.a Pneumonitis (ILD)
XXIV. Interstitial lung disease - Pulmonary infiltrates - Pulmonary fibrosis
XXIV.b Pneumonitis (ILD), acute and/or severe (may cause ARDS)
XXIV. Interstitial lung disease - Pulmonary infiltrates - Pulmonary fibrosis
XXIV.j Organizing pneumonia (OP/BOOP) pattern (an area or areas of consolidation on imaging)
XXVIII. Large airway involvement
XXVIII.a Angioedema (may cause UAO, asphyxia and death)
XXVIII. Large airway involvement
XXVIII.d Vocal cord dysfunction, adduction, closure
XXIX. Small airway involvement
XXIX.a Bronchospasm - Wheezing - Asthma
XXIX. Small airway involvement
XXIX.b Occupational asthma
XXXVI. Autoimmune syndromes - Systemic reactions or conditions
XXXVI.a Autoimmunity - An autoimmune condition (+ANA, +anti-ds-DNA, +ANCAs, other auto-Abs)
XXXVI. Autoimmune syndromes - Systemic reactions or conditions
XXXVI.b Lupus - Lupus syndrome
XXXVI. Autoimmune syndromes - Systemic reactions or conditions
XXXVI.m DRES syndrome - DRESS-like reaction - Drug hypersensitivity syndrome
XXXVI. Autoimmune syndromes - Systemic reactions or conditions
XXXVI.s Dual MPO-/PR3-ANCA systemic disease/vasculitis or pseudovasculitis
XXXVI. Autoimmune syndromes - Systemic reactions or conditions
XXXVI.t Pneumorenal syndrome (w/wo ANCAs)
XXXVI. Autoimmune syndromes - Systemic reactions or conditions
XXXVI.u Pulmonary vasculitis or capillaritis
XXXVIII. Miscellaneous - Varia
XXXVIII.a Upper airway obstruction other than angioedema or hematoma
III. Myocardial ischemia - Coronary artery disease
III.a Coronary artery disease (acute) - Myocardial ischemia/infarction
XI. Pulmonary vasculopathies
XI.a Pulmonary arterial hypertension
XII. Pericardial involvement
XII.n Pleuropericarditis - Pleuropericardial effusion (ANA unknown or negative)
XIV. Pleural involvement
XIV.a Pleural effusion (uni or bilateral) (can accompany ILD induced by the drug)
XVI. Hemorrhage - Bleeding - Hematoma(s)
XVI.e Alveolar hemorrhage (AH), diffuse AH (DAH)
XVI. Hemorrhage - Bleeding - Hematoma(s)
XVI.i Hemoptysis
XVIII. Aortic involvement
XVIII.c Arterial (aorta, limb) vasoconstriction and/or ischemia, acute
XX. Vasculitis
XX.d Vasculitis, pulmonary (w/wo AH), extrathoracic, or systemic: ANCA-positive
XXVIII. Large airway involvement
XXVIII.p Nasal, palatal and/or pharyngeal pathology
XXXI. Eye catchers
XXXI.h Midline destructive lesions
XXXVI. Autoimmune syndromes - Systemic reactions or conditions
XXXVI.s Dual MPO-/PR3-ANCA systemic disease/vasculitis or pseudovasculitis
XXXVI. Autoimmune syndromes - Systemic reactions or conditions
XXXVI.t Pneumorenal syndrome (w/wo ANCAs)
XXXVI. Autoimmune syndromes - Systemic reactions or conditions
XXXVI.u Pulmonary vasculitis or capillaritis
XXXVIII. Miscellaneous - Varia
XXXVIII.d Death following exposure or poisoning
XXXVIII. Miscellaneous - Varia
XXXVIII.q Myopathy-Myositis-Polymyositis
XXXVIII. Miscellaneous - Varia
XXXVIII.y Neutropenia, agranulocytosis (w/wo infection/sepsis)