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XI.a

XI - Pulmonary vasculopathies

Pulmonary arterial hypertension

Last update 17/06/2026

May reverse with drug discontinuation. Generally similar to primary PHTn clinically, hemodynamically and on pathology. PMID 23997051. A few cases are thromboembolic in nature (PMID 24881082). Reviews at PMID 29508628, 30545968

Causative drugs

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